IgG4-Related Sclerosing Pachymeningitis Causing Spinal Cord Compression

Immunoglobulin G (IgG)4-related sclerosing disease is an emerging clinicopathologic entity. It is defined as a systemic disease characterized histopathologically by extensive IgG4-positive plasma cell infiltration of various organs together with T-lymphocyte infiltration.1 Pancreas is the most frequently affected organ. This disease was included within the category of autoimmune pancreatitis before the concept of IgG4-related sclerosing disease...