IgG4-related sclerosing disease: a critical appraisal of an evolving clinicopathologic entity.

Published on Sep 1, 2010in Advances in Anatomic Pathology3.53
· DOI :10.1097/PAP.0b013e3181ee63ce
Wah Cheuk30
Estimated H-index: 30
John K. C. Chan81
Estimated H-index: 81
An elevated serum titer of immunoglobulin G4 (IgG4), the least common (3% to 6%) of the 4 subclasses of IgG, is a surrogate marker for the recently characterized IgG4-related sclerosing disease. The syndrome affects predominantly middle-aged and elderly patients, with male predominance. The patients
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