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Autoinflammatory Diseases in Childhood.

Published on Apr 27, 2020in Balkan Medical Journal1.203
· DOI :10.4274/BALKANMEDJ.GALENOS.2020.2020.4.82
Mehmet Yildiz3
Estimated H-index: 3
(Istanbul University),
Fatih Haşlak1
Estimated H-index: 1
(Istanbul University)
+ 2 AuthorsOzgur Kasapcopur30
Estimated H-index: 30
(Istanbul University)
Abstract
Autoinflammatory diseases are defined as recurrent attacks of systemic inflammation that are often unprovoked (or triggered by a minor event) related to a lack of adequate regulation of the innate immune system. Within the past decade, the list of autoinflammatory diseases has included cryopyrin-associated periodic syndromes, familial Mediterranean fever, mevalonate kinase deficiency, tumor necrosis factor receptor-associated periodic syndrome, hereditary pyogenic disorders, pediatric granulomatous autoinflammatory diseases, idiopathic febrile syndromes (systemic-onset juvenile idiopathic arthritis, PFAPA syndrome), complement dysregulation syndromes and Behcet’s disease. The hereditary autoinflammatory diseases are a group of Mendelian disorders characterized by seemingly unprovoked fever and localized inflammation. Autoinflammatory diseases can activate NOD-like receptors and inflammasome products including especially interleukin 1β. In this review, it focuses on how recent advances have impacted hereditary autoinflammatory diseases.
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