Review paper
IgG4-related disease: a clinical perspective
Abstract
IgG4-related disease (IgG4-RD) is a recently recognized fibro-inflammatory disorder that can affect almost any organ. Common presentations include major salivary and lacrimal gland enlargement, orbital disease, autoimmune pancreatitis, retroperitoneal fibrosis and tubulointerstitial nephritis. The main histopathological features are a dense, polyclonal, lymphoplasmacytic infiltrate rich in IgG4+ plasma cells, storiform fibrosis and obliterative...
Paper Details
Title
IgG4-related disease: a clinical perspective
Published Date
Apr 29, 2020
Journal
Volume
59
Issue
Supplement_3
Pages
iii123 - iii131
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History