38. Simultaneous Living Donor Liver and Kidney Transplantation for Primary Hyperoxaluria Type 1 in a Paediatric Patient

Background and Aims: Primary hyperoxalurias are rare inborn errors of metabolism resulting in increased endogenous production of oxalate that leads to excessive urinary oxalate excretion. There is deficiency of the liver-specific peroxisomal enzyme alanine glyoxylate aminotransferase (AGXT). It is a heterogeneous disease with wide spectrum of clinical, imaging and functional presentation. End Stage Renal Disease (ESRD) is a common presentation....