Muscle imaging in laminopathies: Synthesis study identifies meaningful muscles for follow‐up

Volume: 58, Issue: 6, Pages: 812 - 817
Published: Nov 18, 2018
Abstract
Introduction : Particular fibroadipose infiltration patterns have been recently described by muscle imaging in congenital and later onset forms of LMNA ‐related muscular dystrophies ( LMNA ‐RD). Methods : Scores for fibroadipose infiltration of 23 lower limb muscles in 34 patients with LMNA ‐RD were collected from heat maps of 2 previous studies. Scoring systems were homogenized. Relationships between muscle infiltration and disease duration and...
Paper Details
Title
Muscle imaging in laminopathies: Synthesis study identifies meaningful muscles for follow‐up
Published Date
Nov 18, 2018
Volume
58
Issue
6
Pages
812 - 817
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