Pheochromocytoma in Children and Adolescents With Multiple Endocrine Neoplasia Type 2B

Context Multiple endocrine neoplasia type 2B (MEN2B) is characterized by early-onset medullary thyroid cancer in virtually all cases and a 50% lifetime risk of pheochromocytoma (PHEO) development. The literature on PHEO in patients with MEN2B is limited with most data being reported from adult studies that primarily address MEN2A. Objective The aim of the current study is to describe PHEO development in a cohort of pediatric patients with MEN2B....