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Leptomeningeal form of Immunoglobulin G4-related hypertrophic meningitis with perivascular spread: a case report and review of the literature

Published on Jul 1, 2018in Neuroradiology 2.50
· DOI :10.1007/s00234-018-2028-y
Jasmina Boban2
Estimated H-index: 2
(University of Novi Sad),
Selin Ardalı2
Estimated H-index: 2
(Hacettepe University),
Majda M. Thurnher27
Estimated H-index: 27
(Medical University of Vienna)
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Abstract
Purpose Immunoglobulin G4 (IgG4)-related disease represents a spectrum of fibro-inflammatory disorders that affects various organ systems, including the central nervous system.
  • References (18)
  • Citations (1)
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References18
Newest
Published on Mar 4, 2019in British Journal of Neurosurgery 1.48
Shashank S. Joshi2
Estimated H-index: 2
(Cooper Hospital),
Shilpa Joshi5
Estimated H-index: 5
(Fortis Healthcare)
+ 5 AuthorsKishor A. Choudhari1
Estimated H-index: 1
(Royal Hallamshire Hospital)
AbstractRosai-Dorfman disease (RDD) is a rare condition similar to lymphomas, presenting with cervical lymphadenopathy in young adults. Extra-nodal involvement is relatively common but involvement of the central nervous system (CNS) is rare. Cranial RDD presents with symptoms of raised intracranial pressure, focal or generalised seizures, while spinal RDD presents with pain, peripheral neurological deficits and radiculopathy. In contrast to other similar neoplastic or degenerative conditions aff...
Published on Feb 1, 2017in Immunologic Research 2.61
Armando De Virgilio15
Estimated H-index: 15
(Sapienza University of Rome),
Marco de Vincentiis19
Estimated H-index: 19
(Sapienza University of Rome)
+ 5 AuthorsAntonio Greco19
Estimated H-index: 19
(Sapienza University of Rome)
Hypertrophic pachymeningitis (HP) is a rare disorder that causes thickening of the dura mater. Inflammatory lesions may be located in the cerebral or spinal dura mater or, less frequently, in both locations simultaneously. Numerous clinico-pathological entities cause thickening of the pachymeninges. Indeed, HP is a potential manifestation of many different diseases, but the diagnosis often remains uncertain. Cases in which the pachymeningitis has no known aetiology are termed “idiopathic” HP (IH...
Published on Jun 1, 2016in Multiple Sclerosis Journal 5.65
Renate Engisch1
Estimated H-index: 1
(University of Bern),
David S. Titelbaum1
Estimated H-index: 1
+ 1 AuthorsFrauke Kellner-Weldon6
Estimated H-index: 6
(University of Bern)
Background:Contrast-enhanced (ce) fluid-attenuated inversion recovery magnetic resonance imaging (FLAIR MRI) has recently been shown to identify leptomeningeal pathology in multiple sclerosis.Objective:To demonstrate leptomeningeal enhancement on three-dimensional (3D) FLAIR in a case of Susac’s syndrome.Methods:Leptomeningeal enhancement was correlated with clinical activity over 20 months and compared to retinal fluorescein angiography.Results:The size, number, and location of leptomeningeal e...
Published on Oct 1, 2015in Journal of the Neurological Sciences 2.65
Akiyuki Hiraga12
Estimated H-index: 12
,
Daisuke Ozaki2
Estimated H-index: 2
+ 3 AuthorsSatoshi Kuwabara58
Estimated H-index: 58
(Chiba University)
Published on Jun 1, 2014in JAMA Neurology 12.32
Lucy X. Lu1
Estimated H-index: 1
(Vandy: Vanderbilt University),
Emanuel Della-Torre13
Estimated H-index: 13
(UniSR: Vita-Salute San Raffaele University)
+ 1 AuthorsStephen W. Clark5
Estimated H-index: 5
(Vandy: Vanderbilt University)
Importance IgG4-related hypertrophic pachymeningitis (IgG4-RHP) is an increasingly recognized manifestation of IgG4-related disease, a fibroinflammatory condition that can affect virtually any organ. It is estimated that IgG4-RHP may account for a high proportion of cases of hypertrophic pachymeningitis once considered idiopathic. Objective To summarize the current knowledge on IgG4-RHP including its pathological, clinical, and radiological presentations. Particular emphasis is placed on diagnos...
Published on Feb 11, 2014in Neurology 8.69
Shyamal H. Mehta14
Estimated H-index: 14
(Georgia Regents University),
Jeffrey A. Switzer17
Estimated H-index: 17
(Georgia Regents University)
+ 1 AuthorsAmyn M. Rojiani36
Estimated H-index: 36
(Georgia Regents University)
Immunoglobulin G4–related diseases (IgG4-RD) are a newly recognized category of diseases. CNS involvement in IgG4-RD includes hypophysitis1 and intracranial or spinal manifestations of hypertrophic pachymeningitis.2,3 We present a unique case of rapid cognitive decline due to IgG4-related leptomeningitis. Acknowledgment: The authors thank movement disorders fellows Drs. Daniel Dees and Jill Trumble for assisting with the production of the video of the patient.
Published on Jan 1, 2014in Journal of Neuroimmunology 2.83
Emanuel Della-Torre13
Estimated H-index: 13
(UniSR: Vita-Salute San Raffaele University),
Laura Galli1
Estimated H-index: 1
+ 7 AuthorsMaria Grazia Sabbadini35
Estimated H-index: 35
(UniSR: Vita-Salute San Raffaele University)
Abstract Diagnosis of IgG4-Related Hypertrophic Pachymeningitis (IgG4-HP) relies on meningeal biopsies, because cerebrospinal fluid (CSF) diagnostic biomarkers are lacking. Here, we determined whether IgG4 intrathecal production could distinguish IgG4-HP from other disorders presenting with HP (OHP). In patients with IgG4-HP, the median CSF IgG4 concentration, IgG4 Index and IgG4 Loc were significantly higher than in both controls and OHP. CSF IgG4 levels higher than 2.27 mg/dL identified 100% o...
Published on Nov 1, 2013in The Journal of Rheumatology 3.63
Emanuel Della-Torre13
Estimated H-index: 13
(UniSR: Vita-Salute San Raffaele University),
Gabriella Passerini8
Estimated H-index: 8
(UniSR: Vita-Salute San Raffaele University)
+ 7 AuthorsDiego Franciotta39
Estimated H-index: 39
To the Editor: Immunoglobulin G4-related disease (IgG4-RD) is characterized by fibrous swelling of affected organs, elevations in serum IgG4 concentrations, and responsiveness to glucocorticoid treatment1. Affected tissues display similar histological features: diffuse lymphoplasmacytic infiltration by numerous IgG4-positive plasma cells, occasional eosinophils, storiform fibrosis, and obliterative phlebitis2. IgG4-related hypertrophic pachymeningitis (IgG4-HP) has been identified as a character...
Published on Aug 7, 2012in Neurology 8.69
Kevin Shapiro15
Estimated H-index: 15
,
Riley Bove17
Estimated H-index: 17
+ 2 AuthorsJohn H. Stone67
Estimated H-index: 67
Immunoglobulin G4–related disease (IgG4-RD) is a newly recognized immune-mediated condition that involves multiple organ systems and is frequently characterized by tumefactive lesions. Histopathology demonstrates lymphoplasmacytic infiltrates, storiform fibrosis, and abundant IgG4-positive plasma cells within affected tissues.1 Neurologic manifestations include spinal2,3 and intracranial pachymeningitis.4 One retrospective series suggests that some patients diagnosed with “idiopathic” hypertroph...
Published on Feb 9, 2012in The New England Journal of Medicine 70.67
John H. Stone67
Estimated H-index: 67
,
Yoh Zen62
Estimated H-index: 62
,
Deshpande5
Estimated H-index: 5
Cited By1
Newest
Published on Feb 12, 2019in Neuroradiology 2.50
Stefan Weidauer21
Estimated H-index: 21
(Goethe University Frankfurt),
Christian Hofmann3
Estimated H-index: 3
(Goethe University Frankfurt)
+ 1 AuthorsElke Hattingen30
Estimated H-index: 30
(Goethe University Frankfurt)
Purpose Especially in acute onset of ophthalmoplegia, efficient neuroradiological evaluation is necessary to assist differential diagnosis, clinical course, and treatment options.