Ophthalmological manifestations of IgG4-related disease

Purpose Ig4-related disease is a recently defined entity characterized by a mono or multi organ lymphoplasmocytic infiltrate with IgG4+staining (IgG4+/IgG+ cell ratio>40%), associated with fibrosis or sclerosis and elevated IgG4 serum rate over 135mg/dL. Purpose is to determine the ophthalmological and histological features of IgG4-RD, and to analyse the outcome under treatment. Methods Patients with biopsy-proven IgG4-RD, seen between 2009 and...